英四岁小孩大脑分泌致命毒素 活不过十岁(图)

屈联西

  2011年11月11日 环球网

英国四岁小孩大脑分泌致命毒素

　　Distraught parents have told how their son is slowly being poisoned by his own brain.
　　Blighted by a fatal neurological disorder, four-year-old Morgan Mawson is unlikely to make it to his tenth birthday and is unable to walk or talk.
　　He is one of 200 children in the UK who have infantile Batten's disease which is so rare his parents' chance of meeting and conceiving him was only one in two billion.
　　Both Jenni, 28, and Eddie, 37, from Derby are carriers of the faulty gene which causes Batten's disease - meaning any of their children have a one in four chance of inheriting the condition.
　　At birth there are no symptoms of the disorder so it was only when Morgan failed to develop properly that his parents realised there was something wrong.
　　Doctors told the devastated couple that he was not expected to reach his tenth birthday and that a deadly bodily poison was slowly destroying his brain.
　　Jenni said: “His brain produces a chemical which can be poisonous but Morgan is missing an enzyme which dissolves it - so that poison is killing off his brain.”
　　“It's killing off his nerves in his arms, legs and mouth - it stops him from being able to chew and talking properly.”
　　“His behaviour is regressing. At the moment he wants to throw things everywhere and he wants to put things in his mouth. It's like we've gone back to the baby stage.”
　　Eddie and Jenni have had to quit their jobs to act as full time carers for their children.
　　据英国《每日邮报》11月9日报道，一对伤心欲绝的父母讲述了他们的儿子是如何被自己的大脑慢慢毒害的。
　　4岁的摩根-莫森身患一种致命的神经性疾病，他不大可能会度过自己的第十个生日，并且无法行走或说话。
　　他是英国200个患有婴儿贝敦氏症的小孩之一。这种疾病十分罕见， 罹患它的可能性只有二百万分之一。
　　来自英国德比郡的28岁的珍妮与37岁的艾迪都携带有能导致贝敦氏症的错误基因，这就意味着他们任何一个孩子都有四分之一遗传这种基因的机会。
　　摩根出生时身体并未出现任何紊乱症状，所以只有当他未能正常发育时他的父母才意识到出了问题。
　　医生告诉这对倍感震惊的夫妇，摩根预计活不过十岁。一种致命的身体毒素正慢慢地破坏他的大脑。
　　珍妮说：“他的大脑分泌出了一种有毒的化学物质，但是摩根身体里却没有能够分解它的酶。所以该毒素正在杀死他的大脑。”
　　“这种毒素正在杀死他的手臂、腿部和嘴部的神经，那将会阻碍摩根正常的咀嚼和讲话。”
　　“他的言行正在倒退。现在他想要四处乱丢东西，并且想往嘴巴里塞东西。他就像回到了婴儿阶段。”
　　艾迪和珍妮已经不得不辞去工作在家全职照看他们的孩子。